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KMID : 0882420110810050630
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Korean Journal of Medicine
2011 Volume.81 No. 5 p.630 ~ p.635
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A Case of Peutz-Jeghers Syndrome with Nasal Polyposis
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Lim Sung-Ryoun
Lee Kyoung-Rok
Jeong Hye-Kyong
Kim Hyung-Il
Cho Sung-Bum
Lee Wan-Sik
Joo Young-Eun
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Abstract
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Peutz-Jeghers syndrome (PJS) is a rare autosomal dominant disease characterized by typical mucocutaneous pigmentation and multiple hamartomatous polyps in the gastrointestinal tract. The clinical manifestations of PJS include polyp-induced bowel obstruction, abdominal pain, and gastrointestinal bleeding. The risk of gastrointestinal and extragastrointestinal cancers is also significantly increased in patients with PJS. Nasal polyposis associated with PJS has been described, and is considered an extragastrointestinal manifestation of PJS. We present an unusual case of a patient with PJS and nasal polyposis causing complete unilateral nasal obstructio.
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KEYWORD
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Peutz-Jeghers syndrome, Nasal polyps
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